Mucinous, Tubular and Spindle Cell Carcinoma of the Kidney: a Case Report and Literature Review

Samya Hamad Mehanna; Mariana Sestrem Tortoza Bignelli; Geórgia Travaglia Basso; Alexandre Pastorello; Paulo Eduardo Dietrich Jaworski

doi:10.55825/RECET.SBU.0266

Autores

Samya Hamad Mehanna Faculdade Evangélica Mackenzie do Paraná
Mariana Sestrem Tortoza Bignelli Faculdade Evangélica Mackenzie do Paraná
Geórgia Travaglia Basso Faculdade Evangélica Mackenzie do Paraná
Alexandre Pastorello Hospital Universitário Evangélico Mackenzie do Paraná
Paulo Eduardo Dietrich Jaworski Faculdade Evangélica Mackenzie do Paraná

DOI:

https://doi.org/10.55825/RECET.SBU.0266

Palavras-chave:

Kidney Neoplasms, Renal Cell Carcinoma, Urologic Neoplasms

Resumo

INTRODUCTION: Mucinous, tubular and spindle cell renal carcinoma is an epithelial neoplasm which makes up less than 1% of all renal neoplasms. It is most common in the renal cortex and is characterized by tubules which merge with soft spindle cells in a myxoid stroma. Usually, it is an asymptomatic tumor diagnosed incidentally in imaging exams.

CASE DESCRIPTION: A 67-year-old male patient was attended at a university hospital with diffuse abdominal pain. A computed tomography scan showed a renal mass of approximately 9 cm in its largest dimension. He underwent a nephrectomy, and the histopathological analysis was compatible with mucinous, tubular and spindle cell renal carcinoma.

CONCLUSION: Mucinous tubular and spindle cell carcinoma is a rare neoplasm, with nonspecific findings and, therefore, of a difficult diagnosis. The absence of a spindle component and genetic analysis may help in differential diagnosis, essential to determining the correct prognosis and patient follow-up.

Biografia do Autor

Samya Hamad Mehanna, Faculdade Evangélica Mackenzie do Paraná

Médica pela Universidade Federal do Paraná e Patologista pelo Hospital Universitário Evangélico Mackenzie, hoje atua como pesquisadora e professora na Faculdade Evangélica Mackenzie do Paraná.

Geórgia Travaglia Basso, Faculdade Evangélica Mackenzie do Paraná

Acadêmica de medicina do oitavo período na Faculdade Evangélica Mackenzie do Paraná

Alexandre Pastorello, Hospital Universitário Evangélico Mackenzie do Paraná

Residente de Urologia no Hospital Evangélico Mackenzie do Paraná

Paulo Eduardo Dietrich Jaworski, Faculdade Evangélica Mackenzie do Paraná

Graduação em Medicina pela Universidade Federal do Paraná (2006). Residência Médica em Cirurgia Geral no Hospital Mario Gatti de Campinas (2009-10) e em Urologia no Hospital Universitário Evangélico de Curitiba (2011-13). Professor de Urologia - Faculdade Evangélica Mackenzie do Paraná.

Referências

- WHO Classification of Tumours Editorial Board. Urinary and Male Genital Tumours. WHO Classification of Tumours, 5th Edition, Volume 8. Lyon: International Agency for Research on Cancer; 2022.

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